A rare lung disorder, primary pulmonary hypertension (PPH) is a case where the blood vessels in the lungs become narrow, thus causing high blood pressure in the lungs. Pulmonary arteries are responsible for carrying blood from the body to the lungs. It is in the lungs where carbon dioxide is traded for oxygen.
Also known as idiopathic pulmonary arterial hypertension, PHN is a chronic disease and can lead to heart failure, if not treated on time. The pulmonary arteries are responsible for carrying blood from the body to the lungs, PHN is a disorder that is categorized by an abnormal/irregular increase in pulmonary artery pressure.
Causes of primary pulmonary hypertension
Although causes underlying primary pulmonary hypertension are unknown, there are some forms of PHN that can be linked to defective genes that run in the family. Researchers have established that gene mutation often leads to sensitization of blood vessels and theses can narrow, or constrict when exposed to such factors.
The symptoms of PPH are as follows.
The above-mentioned symptoms usually get worse as the disease progresses.
Less common symptoms of PPH
The signs and symptoms of primary pulmonary hypertension are unrecognizable in its early stages, and often go unnoticed for months. Signs of primary pulmonary hypertension (PPH) is often confused with other conditions that have an effect on the heart and lungs.
While diagnosing pulmonary hypertension, doctors ask about the symptoms and risk factors, including family history and other medical conditions. Having a family member who has or had pulmonary hypertension increases your chances of developing the disease.
PPH is usually diagnosed when a possibility of other diseases have been disregarded. Tests may include:
Treatment for primary pulmonary hypertension
Primary pulmonary hypertension (PPH) is non-curable. However, there are various treatment options available that help in managing the symptoms. Some of these are:
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